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ESID  > 2007


Event report

Report on the 6th ESID Prague Spring Meeting
May 14-15, 2007, Prague
Department of Immunology, 2nd Medical School, Charles University, Prague

On May 14 and 15, the sixth ESID Prague Spring meeting was held at the University Hospital Motol, Prague, Czech Republic. More than thirty participants from 12 countries, namely Czech Republic, Lithuania, Poland, Slovenia, Slovakia, Italy, Netherlands, Portugal, Finland, United Kingdom, Turkey and Iran attended and actively participated in the event; mean age of the participants was less than 35 years (ranging from 23 to 54).

Since its launch in 2002 the Prague ESID meeting has been devoted to the exchange of information on primary immunodeficiencies (PIDs) between Western and Central Europe. This year the main task was to bring together the youngest researchers and clinicians of ESID community. The aim was accomplished through an excellent attendance from EU member states, as well as from our close and further neighbours – Turkey and Iran.

The invited speakers were Andy R. Gennery from BMT Unit in Newcastle General Hospital, UK, Marita Bosticardo from San Raffaele Telethon Institute for Gene Therapy (HSR-TIGET) in Milan, Italy and Miriam van der Burg from Department of Immunology, Erasmus MC, Netherlands.

The introductory lecture of the meeting served as an overview of current progress in haematopoietic stem cell transplantation for primary immunodeficiencies given by Andy R. Gennery, followed by interesting review on gene therapy protocols in Wiskott-Aldrich syndrome presented by Marita Bosticardo. Apart from these surveys relevant case reports flavoured this part of the programme.

Another section of the first day focused on antibody deficiencies. The participants could learn about European study on quality assurance of pneumococcal assays, molecular defects in CVID, clinical relevance of anti-IgA antibodies and clinical data extraction. Case reports on patients with defects in humoural immunity were inspiring elements of this section.

A review on recombination defects in PID was given by Miriam van der Burg at the beginning of the programme on the second day accompanied by instructive case reports on skin presentations in patients with SCID and a follow-up of a patient with Cernunnos deficiency introduced at this meeting last year. An overview of IPEX syndrome and atypical presentation of this syndrome in one family closed this section on severe immunodeficiencies.

A number of talks on chronic granulomatous disease were given by colleagues from Slovenia and Poland. Representatives from Iran informed the audience about phagocyte and complement defects in their homeland.

The first part of the afternoon programme was dedicated to a discussion on current and future activities of ESID Juniors that resulted in a few propositions enhancing future collaboration. Thankworthy projects of enthusiastic team of Prof Vihinen from Finland on information services in primary immunodeficiencies were presented, followed by an overview of PID diseases in Iran.

The last but one section concentrated on unusual and interesting case reports. These cases were highly appreciated and brought to the programme quite practical aspects connecting the bench work with the clinic.

The social programme is an indispensable part of the Prague Spring ESID meeting, as it enables further fostering of close cooperation between all the participants. The relaxing stroll through Prague Castle, dinner in a restaurant in the historical quarter of Prague and a concert in a jazz club in the city centre were all enjoyed by the participants.

The meeting was organized as a part of the activities related to the Day of Immunology, declared by EFIS on 29th April, 2007. It was supported by the Charles University, 2nd Medical School, Prague and by University Hospital in Motol, Prague. Substantial contributions came from pharmaceutical companies Baxter, Grifols, Exbio, Immunotech, Olympus, Baria, ITA-BD, Schoeller and Binding Sites company that provided not only financial support but also books on diagnostics. Thanks to generous help of Talecris three travel grants approved by ESID board could be distributed to Crina Samarghitean (Finland), Lucia Bianchi (Italy) and Ömür Ardeniz (Turkey).

We thank all the participants for their contributions and we are looking forward to next meeting in 2008!

Anna Sediva, Ales Janda
Prague, May 29, 2007


Vital information


Registration form



Date Time Topic Lecturer Materials for download
14.05 13.00 Emerging indications for HSCT in primary immunodeficiency. Andy R. Gennery, Newcastle, Great Britain
14.05 13.45 HSCT in a patient with hyper IgM sydrome - our recent experience. Aleš Janda, Renata Formánková, Prague, Czech Republic
14.05 14.00 Efficacy and safety of hematopoietic stem cell gene therapy for Wiskott Aldrich syndrome. Marita Bosticardo, Milan, Italy
14.05 14.30 Intriguing combination of mutations in WAS patient. Tomáš Freiberger, Brno, Czech Republic
14.05 14.45 Immunoglobulin G response to pneumococcal serotypes and quality assurance for pneumococcal assays in Europe. Daniel Harrison, Oxford, Great Britain
14.05 15.00 Common variable immunodeficiency – atypical presentation. Sara Pereira da Silva, Lisbon, Portugal
14.05 15.10 Molecular analysis of B cell subsets in common variable immunodeficiency. Anna Ridley, Southampton, Great Britain
14.05 15.25 Anti-IgA antibodies: risks and safety of immunoglobulin substitution. Vojtěch Thon, Brno, Czech Republic
14.05 15.40 CVID patients treated in Motol, data extraction for ESID online registry. Daniela Janečková, Aleš Janda, Prague, Czech Republic
14.05 15.50 Osteomalacia in a patient with CVID. Ömür Ardeniz, Ege, Turkey
15.05 09.00 V(D)J recombination defects in primary immunodeficiencies. Mirjam van der Burg, Rotterdam, Netherland
15.05 09.30 Unusal skin presentation in a 4-year-old SCID patient. Edita Heropolitanska-Pliszka, Warsaw, Poland
15.05 09.45 Follow-up of the patient with Cernunnos deficiency. Edita Heropolitanska-Pliszka, Warsaw, Poland
15.05 10.00 A family affected by atypical IPEX syndrome. Eleonora Gambineri, Firenze, Italy
15.05 10.15 FOXP3 gene products analysis in IPEX-like patients: a defect in regulation of expression? Lucia Bianchi, Florence, Italy
15.05 10.45 Severe congenital neutropenia in Iran. Nima Rezaei, Tehran, Iran
15.05 11.00 Clinical and molecular genetic spectrum of Slovenian patients with CGD. Tadej Avčin, Ljubljana, Slovenia
15.05 11.20 Molecular diagnostics of CGD. Maruša Debeljak, Ljubljana, Slovenia
15.05 11.30 Therapeutic management in a boy with XL- CGD complicated by invasive aspergillosis. Maja Klaudel-Dreszler, Warsaw, Poland
15.05 11.40 Proposal for Eastern European register for patients with CGD. Gašper Markelj, Ljubljana, Slovenia
15.05 11.50 Primary complement deficiencies. Maryam Mahmoudi, Tehran, Iran
15.05 13.00 ESID juniors - panel discussion on the activities of this working party. Eleonora Gambineri, Aleš Janda, Firenze, Italy, Prague, Czech Republic
15.05 13.30 Information services for primary immunodeficiencies. Crina Samarghitean, Tampere, Finland
15.05 14.00 The spectrum of primary immunodeficiency diseases in Iran. Nima Rezaei, Tehran, Iran
15.05 14.30 A case you know from the ESID newsletter - any solution? Anna Šedivá, Prague, Czech Republic
15.05 14.45 A 3-year-old well nourished boy with liver abscess. Mojgan Kiani Amin, Qazvin, Iran
15.05 15.00 Progressive T-cell lymphopenia in a child with recurrent fever and multiple neurological abnormalities. Jutte van der Werff ten Bosch, Leiden, Netherland
15.05 15.30 Unknown combined immunodeficiency with T-cell lymphopenia. Rasa Duobiene, Vilnius, Lithuania
15.05 15.45 Suspected transient hemophagocytosis in EBV infection. Pavel Rozsíval, Hradec Králové, Czech Republic






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